Adult Pulmonary Langerhans Cell Histiocytosis with Osseous Involvement: understanding this rare mimic of malignancy
نویسندگان
چکیده
Langerhans cells are dendritic that form the antigenic barrier of human body. They occur in nearly any tissue but most prevalent skin, submucosa bronchial tree, and other mucosae. Cell Histiocytosis (LCH) develops when these damage tissues which they reside through a combination inflammatory monoclonal stimulation. The pulmonary variant LCH involves lung parenchyma creates wide variety disturbances: hypertension both obstructive restrictive disease. Osseous involvement, addition to variant, presents with masses lytic bone lesions, sparks suspicion for malignancy. Early recognition this rare pathology is important as early treatment clinically beneficial. following explores case adult Pulmonary osseous involvement.
منابع مشابه
Adult Langerhans Cell Histiocytosis with Hepatic and Pulmonary Involvement
Langerhans cell histiocytosis (LCH) is a rare proliferative disorder of Langerhans cells of unknown etiology. It can involve multiple organ systems with different clinical presentation, which complicates the diagnosis. It can range from isolated to multisystem disease with different prognosis. Although common among children, liver involvement is relatively rare in adults and frequently overlook...
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Adult pulmonary Langerhans’ cell histiocytosis is a rare disorder of unknown aetiology that occurs predominantly in young smokers, with an incidence peak at 20–40 yrs of age. In adults, pulmonary involvement with Langerhans’ cell histiocytosis usually occurs as a single-system disease and is characterised by focal Langerhans’ cell granulomas infiltrating and destroying distal bronchioles. High-...
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متن کاملPulmonary langerhans cell histiocytosis
Pulmonary Langerhans' cell histiocytosis (PLCH) remains an important diagnostic consideration in the differential diagnosis of diffuse infiltrative lung disease, particular among smokers. This review highlights recent progress in our understanding of the etiology, clinical presentation, and diagnostic and therapeutic approaches to this unusual lung disorder. Evolving studies strongly link the b...
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ژورنال
عنوان ژورنال: Marshall journal of medicine
سال: 2022
ISSN: ['2379-9536']
DOI: https://doi.org/10.33470/2379-9536.1276